Pediatric Cutaneous Mastocytosis: Demographic, Clinical and Histopathological Findings
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Dosyalar
Tarih
2008
Yazarlar
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Galenos Yayincilik
Erişim Hakkı
info:eu-repo/semantics/closedAccess
Özet
Objective: Mastocytosis is a disease characterized by abnormal growth and accumulation of mast cells in one or more organ systems. The skin is the most commonly affected organ. It is aimed to present demographic, clinical and histopathological findings of pediatric patients with cutaneous mastocytosis and a review of the literature in this study. Methods: Demographic, clinical and histopathological data of 14 pediatric patients with cutaneous mastocytosis were retrospectively analyzed. Results: Eleven patients (78.6%) had urticaria pigmentosa, two patients (14.3%) had mastocytoma and one patient (% 7.1) had coexistence of both urticaria pigmentosa and mastocytoma. The onset of the disease occured in the first year of life in 64.3% of patients. Male-female ratio was 1:1.8. Lesions were localised most commonly on the trunk and extremities in patients with urticaria pigmentosa and on the trunk in patients with mastocytoma. Darier's sign was present in 92% of patients. There was one patient with a positive family history. The most frequent complaint was pruritus. Conclusion: Generally our resuls, except for the predominance of girls, are compatible with the studies given earlier.
Açıklama
Anahtar Kelimeler
Childhood, demographic, cutaneous mastocytosis, mastocytoma, nodular mastocytosis, urticaria pigmentosa
Kaynak
Turk Dermatoloji Dergisi-Turkish Journal of Dermatology
WoS Q DeÄŸeri
N/A
Scopus Q DeÄŸeri
Cilt
2
Sayı
3
